Precision Science Group
(PSG)
PCCA mAb
The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene
Alternative Name(s)
PCCAalpha polypeptide; mitochondrial; pccA complementation group; PCCase alpha subunit; PCCase subunit alpha; propanoyl-CoA:carbon dioxide ligase alpha subunit; Propanoyl-CoA:carbon dioxide ligase subunit alpha; propionyl CoA carboxylase, alpha polypeptide; propionyl Coenzyme A carboxylase; propionyl Coenzyme A carboxylase, alpha polypeptide; propionyl-CoA carboxylase alpha chain; Propionyl-CoA carboxylase alpha chain, mitochondrial;PCCA
Application
WB, IF
UNIprot
P05165
clonality
Monoclonal
reactivity
Human,Mouse,Rat
Research area
Fatty Acid Metabolism
source
Mouse
storage
Store at -20℃, stable for one year from the date of shipment.
PCCA mAb